Coexistent mitral and aortic valve atresia with intact ventricular septum in sibs.
نویسندگان
چکیده
serum. A review of the reports on similar cases showed no male preponderance (50%). In contrast, the heterogeneous group ofhypoplastic left heart syndrome showed 64per cent male preponderance. The mean maternal age was 3I years in hypoplastic left heart syndrome, excluding patients with interruption of the aortic arch and mitral and aortic valve atresia where the mean maternal age was lower, 22 and 26
منابع مشابه
Absence of the aortic valve cusps with mitral atresia, normal left ventricle, and intact ventricular septum.
A case of a previously unreported anomaly is presented in which absence of the aortic valve cusps, mitral atresia, a normal left ventricle, and an intact ventricular septum were diagnosed by cross sectional echocardiography. The development of a normal left ventricle, rather than the hypoplastic ventricle usually associated with mitral atresia, is explained by filling of the ventricular cavity ...
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We report a case of aortic atresia with biventricular hypertrophy and death due to cardiac insufficiency (at 5 1/2 days of age). In the necropsy a normally sized left ventricle was observed, with endocardiac fibroelastosis, anomalous mitral arcade, intact interventricular septum and atresia of the aortic valve. The ascending aorta was moderately hypoplasic; there was a foramen ovale and persist...
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A case of pulmonary valve atresia with intact ventricular septum' with long survival in the absence of a patent ductus arteriosus, is presented. The patient, alive at 21 years of age, has the anterior descending branch of the left coronary artery originating from the pulmonary artery. Thus, the pulmonary blood supply is obtained from the right coronary artery via intercoronary anastomoses. No s...
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عنوان ژورنال:
- British heart journal
دوره 36 3 شماره
صفحات -
تاریخ انتشار 1974